Others CSF

Rare conditions where patient exhibit features of raised ICP and show ventriculomegaly on imaging despite very low or negative ICP. Clinical suspicion for low- or negative-pressure hydrocephalus should be high when patients with enlarged ventricles have repeated “shunt failures” that do not improve with shunt revisions. Presence of a CSF leak from the cortical subarachnoid space and/or loss of patency between the ventricles and the cortical subarachnoid space (e.g. arachnoiditis, mechanical) may affect transmante pressure (ventricular pressure—cortical subarachnoid space pressure) and brain turgor, leading to ventriculomegaly and neurological signs

The course is self-limited, manifesting in the first 6 months of life and resolving spontaneously by 2 years of age and thought to be due to transient mismatch in maturation/ability of arachnoid villi to absorb increasing volumes of CSF being produced

Subdural fluid collection resembling CSF, on similar spectrum as subdural effusion and chronic subdural hematoma

Constellation of dementia, incontinence, and gait apraxia with evidence of ventriculomegaly on imaging (without underlying mass lesion) with normal CSF pressure on lumbar puncture