- 80% of encephaloceles
- Subtypes
- Interfrontal
- Anterior fontanelle
- Interparietal
- Uncommon
- Poor prognosis
- Common association with major brain anomalies:
- Dandy-Walker malformation
- Callosal agenesis
- Chiari II malformation
- Holoprosencephaly
- Because of their location there is an increased incidence of sagittal sinus involvement,
- Common location for atretic cephaloceles
- Small, hairless, midline masses associated with a sharply marginated calvarial defect
- High incidence of midline anomalies
- Porencephalies,
- Interhemi-spheric cysts
- Callosal agenesis.
- Temporal
- Posterior fontanelle