Fronto-ethmoidal encephalocele

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General

  • AKA sincipital
  • 15% of encephaloceles;

Due to

  • Failure in the normal regression of a projection of dura that extends from the cranial cavity to the skin through a persistent foramen cecum or fonticulus frontalis.
  • Persistence of this projection of dura may give rise to a dermal sinus tract, which in turn may give origin to a dermoid or epidermoid tumour
notion image

Examination

  • Superficial skin-covered mass
  • Nasal dimple and frequently hypertelorism.

Subtypes of frontoethmoidal cephaloceles are identified by the location of the bony defect

  • Frontonasal cephalocele
    • Location of the bony defect
      • Frontal and nasal bones
    • External defect in the nasion
  • Frontoethmoidal cephalocele
    • Location of the bony defect
      • Frontal, nasal, and ethmoidal bones
    • Defect between nasal bone and nasal cartilage
  • Naso-orbital cephalocele
    • Location of the bony defect:
      • Frontal, lacrimal, and ethmoidal bones extending into the anteromedial portion of the orbit.
    • Defect in the antero-inferior portion of medial orbital wall