Achondroplastic kyphosis

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Status
Done
  • Thoracolumbar kyphosis is the most common sagittal plane deformity among achondroplasic dwarfs.
  • Radiographs show anterior wedging at the apex of the deformity.
  • Clinical features
      • The kyphosis is generally evident at birth, progresses as the child begins to sit
        • Resolves in approximately 70% of cases with ambulation at 12-18 months.
        • Progression can lead to a focal kyphosis and possible neural compression, which may be masked by the lumbar stenosis associated with achondroplasia.
      notion image
  • Treatment
    • Anterior and posterior fusion
      • Indication
        • Progressive deformity
        • Thoracolumbar kyphosis > 50° at age > 5 years
        • Neural compromise attributed to compression in the kyphotic region.