Neurosurgery notes/Tumours/Tumour general/Paediatric Cranial tumours/Paeds sellar tumours

Paeds sellar tumours

View Details
Status
Done
logo
Parent item
Paediatric cranial tumours

Types of tumours

  • Craniopharyngiomas (6-9%)
  • Optic Pathway Hypothalamic Astrocytomas (2-7%)
  • Germinomas (3%)
  • Pituitary Adenomas (1-2%)
  • Dermoids/ Epidermoids
  • Other
    • Meningiomas
    • Haemangiomas
    • Ependymomas
    • Schwannomas
    • Cavernomas

Clinical features associated with pituitary stalk and pineal region lesion

  • Failure to thrive
  • Growth failure
  • Diabetes insipidus
    • Preop DI unusual in craniopharyngioma
    • But common in germ cell tumours involving anterior third ventricle, histiocytosis
  • Delayed puberty
  • Diencephalic syndrome
  • Rarely hypersecretory endocrine fxn
  • Visual problems
  • Parinaud eye signs
- Supranuclear upgaze palsy - Large pupils with light-near dissociation - Lid retraction (Collier sign)
- Supranuclear upgaze palsy
- Large pupils with light-near dissociation
- Lid retraction (Collier sign)
- Normal downgaze - Convergence weakness - Convergence-retraction nystagmus
- Normal downgaze
- Convergence weakness
- Convergence-retraction nystagmus