Dystrophic scoliosis
- Dystrophic scoliosis is characterised by bony dysplasia, including rib penciling, vertebral rotation, vertebral body scalloping, vertebral wedging, widened interpedicular distance, and enlargement of intervertebral foramina.
- Has an early onset and is rapidly progressive, leading to
- Multiplanar deformity
- High incidence of neurological deficits.
- Associated conditions:
- The condition is believed to result from multiple factors such as tumour burden, dural ectasia, abnormal bony metabolism, and biomechanical instability.
- Spinal tumours
- Occur in 1.5% to 24% of NF1 patients
- Higher incidence and tumour burden in those with dystrophic scoliosis.
- Dural ectasia
- Occurs in 29% of NF1 patients with dystrophic scoliosis
- Posing risks for intraoperative and postoperative complications like CSF leaks.
Nondystrophic
- Resembles idiopathic scoliosis.
- Prevalence of Dural Ectasia:
- 11% of Nondystrophic NF1 patients
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